Ebstein's anomaly-How to correct severe anatomical forms of the defect in adults.

We present the case of a 43-year-old female with a severe tricuspid regurgitation due to an Ebstein Anomaly. She was in New York Association Functional Class II, and was still in sinus rhythm despite a hugely dilated right atrium. The preoperative workup included a transthoracic and transesophageal echocardiography which showed a typical aspect of Ebstein anomaly with a 1.5 cm apical displacement of the septal leaflet, dilatation the right atrium and of the right ventricle whose function was decreased. A cardiac catheterization confirmed that the coronary arteries were free of stenotic lesions. The indication to operate the patient was based on the severity of the tricuspid regurgitation, and the symptoms.